Henochschonlein purpura hsp, also known as iga vasculitis, is a disease of the skin, mucous membranes, and sometimes other organs that most commonly affects children. When the blood vessels bleed, you get a rash called purpura. Schonlein henoch enfermedades raras y patologias poco comunes. In the skin, the disease causes palpable purpura small, raised areas of bleeding underneath the skin, often with joint pain and abdominal pain. Symptom, treatment and advice from community members. Hsp can affect blood vessels in the bowel and the kidneys, as well. When blood vessels get inflamed, they can bleed into the skin, causing a. Please use one of the following formats to cite this article in your essay, paper or report. Schonleinhenoch purpura psh is a predominantly pediatric vasculitis with, generally, a benign prognosis. Henochschonlein purpura hsp, also called immunoglobulin a vasculitis igav, is a vascular disease that primarily affects small blood vessels. Apr 17, 20 the vast majority of people with henoch schonlein purpura hsp recover on their own within several weeks. Henoch schonlein purpura hsp affects the blood vessels and causes a spotty rash. Pdf on aug 24, 2010, chetan mukhtyar and others published henochschonlein purpura find, read and cite all the research you need on researchgate. Henochschonlein purpura is a systemic vasculitis mediated by ig a, clinically.
Dec 10, 2018 henoch schonlein purpura hsp, also called immunoglobulin a vasculitis igav, is a vascular disease that primarily affects small blood vessels. A henochschonlein purpura hsp was diagnosed and the patient was. Henochschonlein purpura hsp is a multisystem immunoglobulin amediated vasculitis with a selflimited course affecting the skin, joints, gastrointestinal tract, and kidneys. Pigmented purpuric dermatosis are distinguished from other purpura by size 0. National institutes of health, through the national library of medicine, developed clinicaltrials. Nov 08, 2019 henochschonlein purpura hsp is a rare disease that causes the blood vessels in your skin to become irritated and swollen. Henochschonlein purpura anaphylactoid purpura, vascular purpura internal medicine an acquired form of small vessel vasculitis with igadominant immune deposits affecting small vesselsarteries, capillaries, venules, typically of the skin, gut, and glomeruli, associated with arthralgia andor arthritis. A collection of disease information resources and questions answered by our genetic and rare diseases information specialists for henochschonlein purpura.
However, in adults can adquire greater severity and more frequency of renal involvement. Schonlein henoch enfermedades raras y patologias poco. Henochschonlein purpura definition of henochschonlein. En adultos puede revestir mayor severidad con mayor. Protocolos diagnosticos y terapeuticos en pediatria. The most striking feature of this form of vasculitis is a purplish rash, typically on the lower legs and buttocks. Nov 16, 2018 please use one of the following formats to cite this article in your essay, paper or report. Its incidence is low in childhood with the exception of henoch schonlein purpura hsp and. William heberden, a london physician, described the first cases of henoch schonlein purpura hsp in in describing hsp, heberden wrote of a. Henochschonlein purpura genetic and rare diseases information.1206 1297 1280 493 727 858 1029 1300 1077 186 944 450 378 110 1415 172 896 839 1164 1089 197 21 770 1061 514 1213 942 1197 78 965 905 1201 74 216 411 450 1192